Cloacal exstrophy

From WikiMD's Wellness Encyclopedia

Cloacal exstrophy is a severe birth defect wherein much of the abdominal organs are exposed. It occurs when the baby's abdomen does not close properly during development. This condition is also known as OEIS complex due to the presence of four defects: Omphalocele, Exstrophy of the cloaca, Imperforate anus, and Spinal defects.

Causes[edit | edit source]

The exact cause of cloacal exstrophy is unknown. It is thought to occur randomly during the formation of the urinary tract and rectum. It is not believed to be hereditary.

Symptoms[edit | edit source]

The most obvious symptom of cloacal exstrophy is the exposure of the bladder and intestines at birth. Other symptoms may include:

  • An abnormal anus or rectum
  • Spinal abnormalities
  • Other birth defects

Diagnosis[edit | edit source]

Cloacal exstrophy is usually diagnosed at birth due to the obvious physical abnormalities. Prenatal ultrasound may also detect the condition.

Treatment[edit | edit source]

Treatment for cloacal exstrophy involves multiple surgeries to repair the abdominal wall and reconstruct the bladder and genitalia. Ongoing care is needed to manage potential complications such as urinary tract infections and kidney problems.

Prognosis[edit | edit source]

With proper treatment, individuals with cloacal exstrophy can lead a normal life. However, they may require ongoing medical care and may have issues with continence and sexual function.

See also[edit | edit source]

Cloacal exstrophy Resources

Contributors: Prab R. Tumpati, MD