Leukoencephalopathy with neuroaxonal spheroids

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Leukoencephalopathy with neuroaxonal spheroids
Autosomal dominant - en.svg
This condition is inherited in an autosomal dominant manner



Specialty neurology
















Leukoencephalopathy with neuroaxonal spheroids is a special kind of leukoencephalopathy. It is a cause of severe and subacute dementia. It is inherited, following an autosomal dominant pattern.

It usually presents in childhood but it can also have an adult onset,[1] in which case it can present MRIs that mimic those of progressive multiple sclerosis.[2]

See also[edit]

References[edit]

  1. ↑ "Adult-onset leukoencephalopathy with axonal spheroids and pigmented glia (ALSP): Integrating the literature on hereditary diffuse leukoencephalopathy with spheroids (HDLS) and pigmentary orthochromatic leukodystrophy (POLD)".Journal of Clinical Neuroscience.2018;48(1)
    42–49.doi:10.1016/j.jocn.2017.10.060.PMID:29122458.
  2. ↑ "Sporadic adult-onset leukoencephalopathy with neuroaxonal spheroids mimicking cerebral MS".Neurology.March 2008;70(13 Pt 2)
    1128–33.doi:10.1212/01.wnl.0000304045.99153.8f.PMID:18287567.

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