Multifocal fibrosclerosis

From WikiMD's Food, Medicine & Wellness Encyclopedia

Other Names: Retroperitoneal fibrosis, familial; Mediastinal fibrosis, familial

Multifocal fibrosclerosis and idiopathic fibrosclerosis are disorders of unknown aetiology, characterised by fibrous lesions (co-)occurring at a variety of sites. Known manifestations include retroperitoneal fibrosis, mediastinal fibrosis and Riedel's thyroiditis.

They are now considered to be manifestations of IgG4-related disease.

NIH genetic and rare disease info[edit source]

Multifocal fibrosclerosis is a rare disease.


Multifocal fibrosclerosis Resources
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