Acquired progressive lymphangioma

Acquired Progressive Lymphangioma (APL) is a rare skin disorder characterized by the progressive growth of lymphatic vessels. It is also known as benign lymphangioendothelioma.

Etiology

The exact cause of Acquired Progressive Lymphangioma is unknown. However, it is believed to be associated with the abnormal proliferation of lymphatic endothelial cells. Some researchers suggest that it may be triggered by trauma or inflammation, but this theory is not universally accepted.

Clinical Features

Acquired Progressive Lymphangioma typically presents as clusters of small, translucent, vesicle-like papules. These papules are often filled with lymph fluid and can range in color from clear to red or purple. They are usually found on the trunk or limbs and tend to grow slowly over time.

Diagnosis

Diagnosis of Acquired Progressive Lymphangioma is primarily based on clinical examination and histopathological analysis. Biopsy of the lesion can confirm the diagnosis. The histopathological features include dilated lymphatic channels in the dermis, lined by a single layer of endothelial cells.

Treatment

Treatment options for Acquired Progressive Lymphangioma are limited due to its rarity. Surgical excision is the most common treatment method. Other treatment options include laser therapy, sclerotherapy, and radiotherapy. However, recurrence after treatment is common.

Prognosis

The prognosis for Acquired Progressive Lymphangioma is generally good. Although the condition is progressive, it is benign and does not metastasize. However, it can cause significant cosmetic and psychological distress to the patient.

See Also

• Lymphangioma
• Lymphatic system
• Skin disorder

‎ Template:Rare diseases-stub