Cruveilhier–Baumgarten disease

From WikiMD's Wellness Encyclopedia

Cruveilhier–Baumgarten disease is a rare medical condition characterized by the presence of portal hypertension without the occurrence of liver cirrhosis. The disease was first described by French pathologist Jean Cruveilhier and German pathologist Paul Clemens von Baumgarten, hence the name.

Etymology[edit | edit source]

The disease is named after Jean Cruveilhier (1791–1874), a French pathologist who was a professor of pathological anatomy at the University of Paris, and Paul Clemens von Baumgarten (1848–1928), a German pathologist who was a professor at the University of Tübingen.

Symptoms[edit | edit source]

The main symptom of Cruveilhier–Baumgarten disease is portal hypertension, which is high blood pressure in the portal vein. This can lead to various complications, including esophageal varices, splenomegaly, and ascites. Other symptoms may include caput medusae, which is the appearance of distended and engorged superficial epigastric veins, and a positive Cruveilhier-Baumgarten bruit, which is a venous hum heard in the epigastric region or over the liver.

Diagnosis[edit | edit source]

Diagnosis of Cruveilhier–Baumgarten disease is typically made through a combination of clinical examination and imaging studies. Ultrasound, CT scan, and MRI may be used to visualize the liver and portal vein. In some cases, a liver biopsy may be performed to rule out cirrhosis.

Treatment[edit | edit source]

Treatment for Cruveilhier–Baumgarten disease primarily involves managing the symptoms and complications of portal hypertension. This may include medications to lower blood pressure, endoscopic procedures to treat esophageal varices, and in severe cases, liver transplantation.

Prognosis[edit | edit source]

The prognosis for individuals with Cruveilhier–Baumgarten disease varies depending on the severity of portal hypertension and the presence of other underlying conditions. With appropriate management, many individuals can live a normal lifespan.

See also[edit | edit source]

Cruveilhier–Baumgarten disease Resources
Wikipedia
WikiMD
Navigation: Wellness - Encyclopedia - Health topics - Disease Index‏‎ - Drugs - World Directory - Gray's Anatomy - Keto diet - Recipes

Search WikiMD

Ad.Tired of being Overweight? Try W8MD's physician weight loss program.
Semaglutide (Ozempic / Wegovy and Tirzepatide (Mounjaro / Zepbound) available.
Advertise on WikiMD

WikiMD's Wellness Encyclopedia

Let Food Be Thy Medicine
Medicine Thy Food - Hippocrates

Medical Disclaimer: WikiMD is not a substitute for professional medical advice. The information on WikiMD is provided as an information resource only, may be incorrect, outdated or misleading, and is not to be used or relied on for any diagnostic or treatment purposes. Please consult your health care provider before making any healthcare decisions or for guidance about a specific medical condition. WikiMD expressly disclaims responsibility, and shall have no liability, for any damages, loss, injury, or liability whatsoever suffered as a result of your reliance on the information contained in this site. By visiting this site you agree to the foregoing terms and conditions, which may from time to time be changed or supplemented by WikiMD. If you do not agree to the foregoing terms and conditions, you should not enter or use this site. See full disclaimer.
Credits:Most images are courtesy of Wikimedia commons, and templates Wikipedia, licensed under CC BY SA or similar.

Contributors: Prab R. Tumpati, MD