Endolymphatic sac tumor

Endolymphatic Sac Tumor is a rare, slow-growing tumor that originates in the endolymphatic sac, a part of the inner ear. These tumors are associated with Von Hippel-Lindau disease, a genetic condition that causes tumors and cysts to grow in the body.

Symptoms

The symptoms of an endolymphatic sac tumor can vary, but often include:

• Hearing loss
• Tinnitus (ringing in the ears)
• Vertigo (a sense of spinning)
• Facial nerve paralysis

Diagnosis

Diagnosis of an endolymphatic sac tumor typically involves a combination of medical history, physical examination, and imaging tests such as MRI or CT scan.

Treatment

Treatment options for endolymphatic sac tumors include:

• Surgery to remove the tumor
• Radiation therapy
• Chemotherapy

Prognosis

The prognosis for individuals with an endolymphatic sac tumor varies depending on the size and location of the tumor, as well as the individual's overall health.

See Also

• Von Hippel-Lindau disease
• Inner ear
• Hearing loss
• Tinnitus
• Vertigo
• Facial nerve paralysis
• MRI
• CT scan
• Surgery
• Radiation therapy
• Chemotherapy

• Post contrast T1 weighted MRI demonstrates intense enhancement of both the eye and the endolymphatic sac tumor.
  Post contrast T1 weighted MRI demonstrates intense enhancement of both the eye and the endolymphatic sac tumor.
• CT through the petrous ridge showing endolymphatic sac tumor in Von Hippel-Lindau disease.
  CT through the petrous ridge showing endolymphatic sac tumor in Von Hippel-Lindau disease.
• Ear Endolymphatic Sac Tumor H and E Low power.
  Ear Endolymphatic Sac Tumor H and E Low power.
• Ear Endolymphatic Sac Tumor H & E High power.
  Ear Endolymphatic Sac Tumor H & E High power.