OHVIRA

OHVIRA or Obstructed Hemivagina and Ipsilateral Renal Anomaly is a rare congenital condition that affects the female reproductive and urinary systems. It is also known as Herlyn-Werner-Wunderlich syndrome.

Overview

OHVIRA is characterized by a triad of anomalies: a double uterus (uterus didelphys), an obstructed hemivagina, and an ipsilateral renal anomaly. The condition is usually diagnosed after menarche, when symptoms such as pelvic pain and a mass become apparent. However, it can also be diagnosed in adulthood.

Symptoms

The symptoms of OHVIRA can vary depending on the extent of the obstruction and the presence of other anomalies. Common symptoms include:

• Pelvic pain
• Dysmenorrhea (painful periods)
• Abnormal vaginal discharge
• Hematocolpos (accumulation of menstrual blood in the vagina)

Diagnosis

Diagnosis of OHVIRA is typically made through imaging studies such as ultrasound, MRI, or CT scan. These can reveal the characteristic triad of anomalies. In some cases, laparoscopy may be used to confirm the diagnosis.

Treatment

Treatment of OHVIRA typically involves surgery to remove the obstruction and allow normal menstrual flow. This can often be done through minimally invasive techniques. In some cases, additional surgeries may be needed to address other anomalies.

Prognosis

With appropriate treatment, the prognosis for individuals with OHVIRA is generally good. Most are able to have normal menstrual cycles and fertility following surgery.

See also

• Uterus didelphys
• Dysmenorrhea
• Hematocolpos

References

OHVIRA Resources
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