Waldmann

Waldmann's disease (also known as Primary intestinal lymphangiectasia) is a rare disorder characterized by enlargement and leakage of the lymph vessels in the small intestine. The disease was first described by the German physician Thomas Waldmann in 1961.

Symptoms

The most common symptoms of Waldmann's disease include protein-losing enteropathy, edema, lymphopenia, and hypogammaglobulinemia. Other symptoms may include malabsorption, malnutrition, and immunodeficiency due to loss of lymph fluid.

Causes

The exact cause of Waldmann's disease is unknown. However, it is believed to be caused by a congenital defect in the lymphatic system. The disease is not inherited and occurs sporadically.

Diagnosis

Diagnosis of Waldmann's disease is based on the clinical symptoms and confirmed by endoscopy and biopsy of the small intestine. Other diagnostic tests may include blood tests, stool tests, and imaging studies.

Treatment

Treatment of Waldmann's disease is aimed at managing the symptoms and preventing complications. This may include a low-fat diet, protein supplements, and medications to reduce lymph fluid leakage. In severe cases, surgery may be required.

Prognosis

The prognosis for individuals with Waldmann's disease varies. Some individuals may have a normal life expectancy with appropriate treatment, while others may experience serious complications and reduced life expectancy.

See also

• Lymphatic system
• Lymphangiectasia
• Protein-losing enteropathy

References

Waldmann Resources
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