Dentin dysplasia

A rare genetic disorder affecting dental tissues

Classification
External resources

Dentin Dysplasia

Radiographic image showing dentin dysplasia

Dentin dysplasia is a rare genetic disorder that affects the development of dentin, the hard tissue that forms the bulk of a tooth. This condition is characterized by abnormal dentin structure, leading to various dental problems.

Classification

Dentin dysplasia is classified into two main types:

Type I (Radicular Dentin Dysplasia)

Type I, also known as radicular dentin dysplasia, primarily affects the roots of the teeth. The roots are short, blunt, or absent, which can lead to premature tooth loss. The crowns of the teeth may appear normal, but the root structure is compromised.

Type II (Coronal Dentin Dysplasia)

Type II, or coronal dentin dysplasia, affects the crowns of the teeth. The teeth may have a normal root structure, but the crowns exhibit abnormal dentin formation. This can result in amber-colored teeth and pulp stones.

Clinical Features

Patients with dentin dysplasia may present with the following clinical features:

• Short or absent roots
• Early loss of teeth
• Discoloration of teeth
• Pulpal obliteration
• Periapical radiolucencies

Diagnosis

Diagnosis of dentin dysplasia is primarily based on clinical examination and radiographic findings. Dental radiography is essential to identify the characteristic root and crown abnormalities associated with the condition.

Treatment

There is no cure for dentin dysplasia, but treatment focuses on managing symptoms and preserving dental function. This may include:

• Regular dental check-ups
• Preventive dental care
• Restorative procedures to address tooth loss or damage

Related Pages

• Dentinogenesis imperfecta
• Amelogenesis imperfecta
• Tooth development