Absent pulmonary valve syndrome

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Absent pulmonary valve syndrome is a congenital heart defect that occurs when the flaps of the pulmonary valve do not develop or are severely underdeveloped (hypoplasia) resulting in aneurysms (dilation) of the pulmonary arteries and softening of the trachea and bronchi (tracheobronchomalacia). Usually, APVS occurs together with other congenital heart defects, most commonly ventricular septal defect and right ventricular outflow tract obstruction. It is sometimes considered a variant of Tetralogy of Fallot.^[1]

References[edit]

↑ Nölke, Lars."The Lecompte Maneuver for Relief of Airway Compression in Absent Pulmonary Valve Syndrome".The Annals of Thoracic Surgery.May 2006;81(5)
1802–1807.doi:10.1016/j.athoracsur.2005.12.001.PMID:16631676.

Congenital heart defects

Heart septal defect

Aortopulmonary septal defect	* Double outlet right ventricle Taussig–Bing syndrome Transposition of the great vessels dextro levo Persistent truncus arteriosus Aortopulmonary window
Atrial septal defect	* Sinus venosus atrial septal defect Lutembacher's syndrome
Ventricular septal defect	* Tetralogy of Fallot
Atrioventricular septal defect	* Ostium primum
Consequences	* Cardiac shunt Cyanotic heart disease Eisenmenger syndrome

Valvular heart disease

Right	* pulmonary valves stenosis insufficiency absence tricuspid valves atresia regurgitation stenosis Ebstein's anomaly
Left	* aortic valves stenosis insufficiency bicuspid mitral valves stenosis regurgitation

Other

* Underdeveloped heart chambers

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Diagram of the human heart

Diagram of the human heart

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