Erythrokeratoderma ''en cocardes''
Alternate names
Erythrokeratoderma "en cocardes"; Degos genodermatosis "en cocardes"; Erythrokeratoderma en cocardes (Degos syndrome); Degos 'en cocarde' erythrokeratoderma
Definition
A rare, genetic, epidermal disorder characterized by intermittent (remitting and recurring), annular, polycyclic, target-like (or 'en cocardes') plaques with concentric rings of scaling erythema occurring on the extremities, flexural areas, and trunk. Concurrent erythrokeratoderma variabilis-like scaly plaques are commonly found in other parts of the body.
NIH genetic and rare disease info
Erythrokeratoderma ''en cocardes'' is a rare disease.
Resources
Frequently asked questions
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