Morvan's fibrillary chorea
Definition
Morvan syndrome is a rare, life-threatening, acquired neurologic disease characterized by neuromyotonia, dysautonomia and encephalopathy with severe insomnia. Signs involving central (e.g. hallucinations, confusion, amnesia, myoclonus), autonomic (e.g. variations in blood pressure, hyperhidrosis) and peripheral (e.g. painful cramps, myokymia) hyperactivity, as well as systemic manifestations (such as weight loss, pruritus, fever), are reported. Thymoma is present in some cases.
NIH genetic and rare disease info
Morvan's fibrillary chorea is a rare disease.
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Frequently asked questions
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Semaglutide (Ozempic / Wegovy and Tirzepatide (Mounjaro) available.
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Contributors: Prab R. Tumpati, MD