Kozlowski-Krajewska syndrome

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Kozlowski-Krajewska syndrome
Synonyms Kozlowski-Krajewska syndrome
Pronounce N/A
Specialty N/A
Symptoms Short stature, skeletal dysplasia, dwarfism
Complications Joint pain, mobility issues
Onset Congenital
Duration Lifelong
Types N/A
Causes Genetic mutation
Risks Family history
Diagnosis Clinical examination, genetic testing
Differential diagnosis Achondroplasia, hypochondroplasia
Prevention None
Treatment Physical therapy, orthopedic surgery
Medication Pain management
Prognosis Variable
Frequency Rare
Deaths N/A


Alternate names

Intellectual disability-polydactyly-uncombable hair syndrome

Definition

Intellectual disability-polydactyly-uncombable hair syndrome is a multiple congenital anomalies/dysmorphic syndrome characterized by intellectual disability, postaxial polydactyly, phalangeal hypoplasia, 2-3 toe syndactyly, uncombable hair and facial dysmorphism (including frontal bossing, hypotelorism, narrow palpebral fissures, nasal bridge and lips, prominent nasal root, large abnormal ears with prominent antihelix, poorly folded helix, underdeveloped lobule and antitragus, and micrognathia evolving into prognatism). Cryptorchidism, conductive hearing loss and progressive thoracic kyphosis were also reported.

NIH genetic and rare disease info

Kozlowski-Krajewska syndrome is a rare disease.


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