Poikiloderma vasculare atrophicans

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Poikiloderma vasculare atrophicans
Poikiloderma vasculare atrophicans 2.JPG
Synonyms
Pronounce
Specialty Dermatology
Symptoms Skin atrophy, telangiectasia, hyperpigmentation, hypopigmentation
Complications
Onset
Duration
Types
Causes
Risks
Diagnosis Clinical diagnosis, skin biopsy
Differential diagnosis Poikiloderma of Civatte, scleroderma, lupus erythematosus
Prevention
Treatment
Medication
Prognosis
Frequency
Deaths


Diagram of skin layers
Illustration of skin structure

Poikiloderma vasculare atrophicans (PVA) is a rare dermatological condition characterized by skin atrophy, telangiectasia, and hyperpigmentation. It is a form of poikiloderma, a group of conditions that involve changes in skin color and texture.

Etiology[edit | edit source]

The exact cause of PVA is unknown. However, it is believed to be associated with various underlying conditions such as cutaneous T-cell lymphoma, dermatomyositis, and scleroderma. Some researchers suggest that it may be an autoimmune response, but this theory is not universally accepted.

Symptoms[edit | edit source]

The primary symptoms of PVA include changes in skin color (hyperpigmentation and hypopigmentation), skin atrophy, and telangiectasia. These changes typically occur on the neck, chest, and limbs. The skin may also become dry and scaly. In some cases, patients may experience itching or discomfort.

Diagnosis[edit | edit source]

Diagnosis of PVA is primarily based on clinical examination and the patient's medical history. Dermoscopy and skin biopsy may be used to confirm the diagnosis and rule out other conditions.

Treatment[edit | edit source]

There is currently no cure for PVA. Treatment is primarily aimed at managing symptoms and preventing complications. This may include the use of topical corticosteroids, photoprotection, and emollients. In severe cases, immunomodulatory therapy may be considered.

Prognosis[edit | edit source]

The prognosis for PVA varies depending on the underlying cause and the severity of the condition. With appropriate management, most patients can lead a normal life. However, the condition can cause significant cosmetic concerns and may impact the patient's quality of life.

See also[edit | edit source]

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Contributors: Prab R. Tumpati, MD