Dentatorubral atrophy

Ramsay Hunt syndrome type 1

Other names

It is alternatively called dyssynergia cerebellaris myoclonica, dyssynergia cerebellaris progressiva, dentatorubral degeneration, or Ramsay Hunt cerebellar syndrome.

Symptoms

Symptoms include seizures, tremor, and reduced muscle coordination.

Onset

Onset of the disorder generally occurs in early adulthood. Tremor may begin in one extremity and later spread to involve the entire voluntary muscular system. Arms are usually more affected than legs. Some of the cases are due to mitochondrial abnormalities.

Treatment

Treatment of Dyssynergia Cerebellaris Myoclonica is symptomatic. Myoclonus and seizures may be treated with drugs like valproate.

Prognosis

The progression of the disorder is usually 10 years or longer

External links

• dyssynergia at NINDS