Dyssynergia Cerebellaris Myoclonica

For other uses, see Ramsay Hunt syndrome.

Also called Ramsay Hunt syndrome type 1, Dyssynergia Cerebellaris Myoclonica refers to a collection of rare, degenerative, neurological disorders characterized by epilepsy, cognitive impairment, myoclonus, and progressive ataxia. Symptoms include seizures, tremor, and reduced muscle coordination.

Onset

Onset of the disorder generally occurs in early adulthood. Tremor may begin in one extremity and later spread to involve the entire voluntary muscular system. Arms are usually more affected than legs. Some of the cases are due to mitochondrial abnormalities.

Treatment

Treatment of Dyssynergia Cerebellaris Myoclonica is symptomatic. Myoclonus and seizures may be treated with drugs like valproate.

Prognosis

The progression of the disorder is usually 10 years or longer.

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Classification	ICD-10: G11.1 ICD-9-CM: 334.2 OMIM: 213400 MeSH: D002527 DiseasesDB: 30054

• dyssynergia at NINDS